Graduate course
Venue: Hotel Valpré, Ecully (near Lyon), FranceOpening: Sept. 13th 2017, 2:00 pm
Closing: Sept. 14th 2017, 5:00 pm
Wednesday Sept. 13 afternoon:
Basic aspects of lysosomal biology
2.00 pmBruno Gasnier & Marie Vanier
Introductory remarks
2:15 – 3:00 pm
Thomas Braulke (Universitäts Klinikum Hamburg-Eppendorf, Germany)
Biogenesis of lysosomes
3:00 – 3:45 pm
Carmine Settembre (Telethon Institute of Genetics and Medicine, Pozzuoli, Italy) Autophagy and lysosomal adaptation
3:45 – 4:15 pm
Coffee break
4:15 – 5:00 pm
Paul Saftig (Kiel University, Germany)
Lysosomal membrane proteins
5:00 – 5:45 pm
Bruno Gasnier (Paris Descartes University, France)
Lysosomal channels and transporters
Thursday Sept. 14 morning
Translational and clinical aspects
8:45 – 9:30 pm Tim Cox (University of Cambridge, UK)
Lysosomal lipid degradation and lipid storage diseases
9:30 – 10:15 pm
Marie Vanier (Inserm, Lyon, France)
Niemann Pick C disease
10:15 – 10:45 pm
Coffee break
10:45 – 11:30 pm
To be confirmed: Angela Schultz (Universitäts Klinikum Hamburg-Eppendorf, Germany)
Pathology and treatment of Neuronal Ceroid Lipofuscinoses
11:30 – 12:15 pm
Brian Bigger (University of Manchester)
Therapy of lysosomal storage diseases
Thursday Sept. 14 afternoon
Journal club
Small groups of graduate students & postdocs from distinct laboratories formed before the courseRecent papers based on lecturers’ suggestions sent several weeks before the course
1:30 pm – ~3 pm
Each subgroup finalizes its presentation
~3 pm – 5:00 pm
Oral presentations (15-min talk + 15 min questions)